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Cellosaurus STHdhQ109 (CVCL_M589)

[Text version]
Cell line name STHdhQ109
Synonyms STHdhQ109/Q109
Accession CVCL_M589
Resource Identification Initiative To cite this cell line use: STHdhQ109 (RRID:CVCL_M589)
Comments Characteristics: From a transgenic mouse containing homozygous HTT loci with a humanized exon 1 containing 109 polyglutamine repeats (PubMed=21985783).
Genetic integration: Method=Transduction; Gene=UniProtKB; P03070; SV40 large T antigen.
Genetic integration: Method=Transduction; Gene=UniProtKB; P00552; Transposon Tn5 neo.
Transformant: NCBI_TaxID; 1891767; Simian virus 40 (SV40) (Note=tsA58).
Derived from site: In situ; Brain, forebrain, striatum; UBERON=UBERON_0002435.
Cell type: Neuron; CL=CL_0000540.
Species of origin Mus musculus (Mouse) (NCBI Taxonomy: 10090)
Age at sampling 14FD
Category Transformed cell line
Publications

PubMed=21985783; DOI=10.1172/JCI57552; PMCID=PMC3223861
Keryer G., Pineda J.R., Liot G., Kim J., Dietrich P., Benstaali C., Smith K., Cordelieres F.P., Spassky N., Ferrante R.J., Dragatsis I., Saudou F.
Ciliogenesis is regulated by a huntingtin-HAP1-PCM1 pathway and is altered in Huntington disease.
J. Clin. Invest. 121:4372-4382(2011)

Cross-references
Encyclopedic resources Wikidata; Q54970578
Entry history
Entry creation05-Nov-2013
Last entry update10-Sep-2024
Version number11