ID   SU-DIPG-XXI
AC   CVCL_C1MX
SY   SU-DIPG-21; SJHGG054836
DR   Wikidata; Q114313060
RX   PubMed=28823557;
RX   PubMed=33319914;
RX   PubMed=34215733;
CC   Doubling time: 4.6 days (PubMed=34215733).
CC   Sequence variation: Mutation; HGNC; 4776; H3C2; Simple; p.Lys28Met (c.83A>T) (H3.1K27M); Zygosity=Unspecified (PubMed=28823557).
CC   Derived from site: In situ; Brainstem, pons; UBERON=UBERON_0000988.
ST   Source(s): PubMed=28823557
ST   Amelogenin: X,Y
ST   CSF1PO: 11,12
ST   D13S317: 8,13
ST   D16S539: 10
ST   D21S11: 30,32
ST   D5S818: 10,11
ST   D7S820: 8,9
ST   TH01: 6
ST   TPOX: 8,12
ST   vWA: 16,19
DI   NCIt; C94764; Diffuse intrinsic pontine glioma
DI   ORDO; Orphanet_497188; Diffuse intrinsic pontine glioma
OX   NCBI_TaxID=9606; ! Homo sapiens (Human)
SX   Male
AG   8Y
CA   Cancer cell line
DT   Created: 22-09-22; Last updated: 29-06-23; Version: 4
//
RX   PubMed=28823557; DOI=10.1016/j.cell.2017.07.016; PMCID=PMC5587159;
RA   Qin E.Y., Cooper D.D., Abbott K.L., Lennon J., Nagaraja S., Mackay A.,
RA   Jones C., Vogel H., Jackson P.K., Monje M.;
RT   "Neural precursor-derived pleiotrophin mediates subventricular zone
RT   invasion by glioma.";
RL   Cell 170:845-859.e19(2017).
//
RX   PubMed=33319914; DOI=10.1093/gigascience/giaa136; PMCID=PMC7736793;
RA   Sanders L.M., Cheney A., Seninge L., van den Bout A., Chen M.,
RA   Beale H.C., Kephart E.T., Pfeil J., Learned K., Lyle A.G., Bjork I.,
RA   Haussler D., Salama S.R., Vaske O.M.;
RT   "Identification of a differentiation stall in epithelial mesenchymal
RT   transition in histone H3-mutant diffuse midline glioma.";
RL   GigaScience 9:giaa136.1-giaa136.14(2020).
//
RX   PubMed=34215733; DOI=10.1038/s41467-021-24168-8; PMCID=PMC8253809;
RA   He C., Xu K., Zhu X.-Y., Dunphy P.S., Gudenas B., Lin W.-W., Twarog N.,
RA   Hover L.D., Kwon C.-H., Kasper L.H., Zhang J.-Y., Li X.-Y., Dalton J.,
RA   Jonchere B., Mercer K.S., Currier D.G., Caufield W., Wang Y.-Z., Xie J.,
RA   Broniscer A., Wetmore C., Upadhyaya S.A., Qaddoumi I., Klimo P.,
RA   Boop F., Gajjar A., Zhang J.-H., Orr B.A., Robinson G.W., Monje M.,
RA   Freeman B.B. 3rd, Roussel M.F., Northcott P.A., Chen T.-S., Rankovic Z.,
RA   Wu G., Chiang J.C.-H., Tinkle C.L., Shelat A.A., Baker S.J.;
RT   "Patient-derived models recapitulate heterogeneity of molecular
RT   signatures and drug response in pediatric high-grade glioma.";
RL   Nat. Commun. 12:4089.1-4089.17(2021).
//