ID   IB3-1/C38
AC   CVCL_4462
SY   C38
DR   BTO; BTO:0004447
DR   CLO; CLO_0002118
DR   ATCC; CRL-2779
DR   ATCC; JHU-54
DR   BioSample; SAMN03471787
DR   Wikidata; Q54897164
RX   PubMed=1380129;
RX   PubMed=7679117;
RX   PubMed=18441018;
CC   Genetic integration: Method=Transfection/transduction; Gene=HGNC; 1884; CFTR.
CC   Genetic integration: Method=Transfection/transduction; Gene=UniProtKB; P00552; Transposon Tn5 neo.
CC   Transformant: Ad12-SV40 hybrid virus.
CC   Discontinued: ATCC; CRL-2779; true.
CC   Discontinued: ATCC; JHU-54; true.
ST   Source(s): ATCC=CRL-2779
ST   Amelogenin: X
ST   CSF1PO: 10,11
ST   D13S317: 8,12,13
ST   D16S539: 9,11
ST   D5S818: 11,12,13
ST   D7S820: 11,12
ST   TH01: 8,9.3
ST   TPOX: 8,9
ST   vWA: 15,18
DI   NCIt; C2975; Cystic fibrosis
DI   ORDO; Orphanet_586; Cystic fibrosis
OX   NCBI_TaxID=9606; ! Homo sapiens (Human)
HI   CVCL_0338 ! IB3-1
SX   Male
AG   7Y
CA   Transformed cell line
DT   Created: 04-04-12; Last updated: 10-09-24; Version: 13
//
RX   PubMed=1380129; DOI=10.1038/358581a0;
RA   Egan M., Flotte T.R., Afione S.A., Solow R., Zeitlin P.L., Carter B.J.,
RA   Guggino W.B.;
RT   "Defective regulation of outwardly rectifying Cl- channels by protein
RT   kinase A corrected by insertion of CFTR.";
RL   Nature 358:581-584(1992).
//
RX   PubMed=7679117; DOI=10.1016/S0021-9258(18)53762-5;
RA   Flotte T.R., Afione S.A., Solow R., Drumm M.L., Markakis D.,
RA   Guggino W.B., Zeitlin P.L., Carter B.J.;
RT   "Expression of the cystic fibrosis transmembrane conductance regulator
RT   from a novel adeno-associated virus promoter.";
RL   J. Biol. Chem. 268:3781-3790(1993).
//
RX   PubMed=18441018; DOI=10.1194/jlr.M700388-JLR200; PMCID=PMC2444007;
RA   Andersson C., Al-Turkmani M.R., Savaille J.E., Alturkmani R.,
RA   Katrangi W., Cluette-Brown J.E., Zaman M.M., Laposata M.,
RA   Freedman S.D.;
RT   "Cell culture models demonstrate that CFTR dysfunction leads to
RT   defective fatty acid composition and metabolism.";
RL   J. Lipid Res. 49:1692-1700(2008).
//